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paediatrics cardiology

RACHS-1 — Risk Adjustment for Congenital Heart Surgery

Six-category consensus risk adjustment for in-hospital mortality after congenital heart surgery in children (Jenkins 2002). Use the category of the most complex procedure. For comparing groups, not individual prognosis.

Score interpretation

Category 1 — Mortality 0.4% 1

In-hospital mortality in the Pediatric Cardiac Care Consortium data (Jenkins 2002); current outcomes are lower.

→ Routine paediatric cardiac surgery pathway.

Category 2 — Mortality 3.8% 2

In-hospital mortality in the Pediatric Cardiac Care Consortium data (Jenkins 2002); current outcomes are lower.

→ Routine paediatric cardiac surgery pathway.

Category 3 — Mortality 8.5% 3

In-hospital mortality in the Pediatric Cardiac Care Consortium data (Jenkins 2002); current outcomes are lower.

→ PICU after surgery with extended monitoring; multidisciplinary planning.

Category 4 — Mortality 19.4% 4

In-hospital mortality in the Pediatric Cardiac Care Consortium data (Jenkins 2002); current outcomes are lower.

→ Tertiary congenital cardiac centre with ECMO availability; pre-operative MDT and parental counselling.

Category 5 — Too Few Cases to Estimate Mortality 5

In-hospital mortality in the Pediatric Cardiac Care Consortium data (Jenkins 2002); current outcomes are lower.

→ Tertiary congenital cardiac centre with ECMO availability; pre-operative MDT and parental counselling.

Category 6 — Mortality 47.7% 6

In-hospital mortality in the Pediatric Cardiac Care Consortium data (Jenkins 2002); current outcomes are lower.

→ Tertiary congenital cardiac centre with ECMO availability; pre-operative MDT and parental counselling.

Interpretation bands for the RACHS-1. Apply clinical judgement and local guidance.

References

Related

Curated clinical cross-links plus same-class fallbacks.

Decision support only — verify against a current formulary, NICE, or your local guideline before clinical use.