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siRNA targeting glycolate oxidase (HAO1)

Lumasiran

Brand names: Oxlumo

Adult dose

Dose: Weight-based SC monthly for 3 doses then quarterly maintenance
Route: SC
Frequency: monthly then q3m

Clinical pearls

  • Primary hyperoxaluria type 1 — specialist metabolic/nephrology

Contraindications

  • Hypersensitivity

Side effects

  • Injection site reactions
  • Abdominal pain

Monitoring

  • Urinary oxalate
  • Renal function

Reference: BNF; NICE HST; SmPC; https://bnf.nice.org.uk/drugs/lumasiran/. Verify against your local formulary and the latest BNF before prescribing.