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paediatrics infectious-disease rheumatology

Kawasaki Disease Diagnostic Criteria

American Heart Association (AHA) diagnostic criteria for Kawasaki Disease (KD). Fever ≥5 days PLUS ≥4 principal features required for classic KD. Guides IVIG and aspirin therapy.

Score interpretation

Classic Kawasaki Disease (with fever)

→ Classic Kawasaki Disease: Fever ≥5 days + ≥4 criteria met. Treat immediately: IVIG 2 g/kg single infusion over 10–12 hours + aspirin 30–50 mg/kg/day in 4 divided doses. Echocardiogram at diagnosis; repeat at 2 and 6 weeks. Paediatric cardiology urgent review.

Incomplete Kawasaki Disease — Assess Further

→ Incomplete (atypical) KD possible: Fever ≥5 days with 2–3 criteria. Measure CRP, ESR, albumin, ALT, WBC, haemoglobin, platelets, urinalysis. If CRP ≥3 mg/dL or ESR ≥40 mm/hr with supplemental lab criteria — treat as KD. Echocardiogram. Paediatric cardiology/immunology review.

KD Unlikely

→ Kawasaki Disease unlikely with <2 criteria (in febrile child). Consider alternative diagnoses: viral exanthem, scarlet fever, adenovirus, SJS, systemic JIA. If high clinical suspicion, consult paediatric infectious disease.

Interpretation bands for the Kawasaki Criteria. Apply clinical judgement and local guidance.

References

Related

Curated clinical cross-links plus same-class fallbacks.

Decision support only — verify against a current formulary, NICE, or your local guideline before clinical use.