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paediatrics rheumatology cardiology

Kawasaki Disease Diagnostic Criteria

Diagnoses Kawasaki disease using AHA/JCS classic and incomplete criteria. Guides IVIG and aspirin therapy to prevent coronary artery aneurysms.

Score interpretation

Kawasaki unlikely or incomplete criteria

→ Consider alternative diagnosis; if incomplete Kawasaki suspected: CRP, ESR, echo; consult paediatric rheumatology; treat if 2-3 criteria + abnormal echo or elevated CRP/ESR

Classic Kawasaki disease (fever + 4 of 5 criteria)

→ Urgent IVIG 2g/kg single infusion; aspirin 30-50mg/kg/day (high dose until afebrile, then 3-5mg/kg/day); echocardiogram; paediatric cardiology review

Definite Kawasaki (fever + 5 criteria)

→ IVIG 2g/kg urgently; high-dose aspirin; echocardiogram at diagnosis, 2 weeks, 6-8 weeks; if IVIG-resistant (fever persists 36h): repeat IVIG or infliximab or corticosteroids; coronary artery aneurysm monitoring

Interpretation bands for the Kawasaki Disease. Apply clinical judgement and local guidance.

References

Related

Curated clinical cross-links plus same-class fallbacks.

Decision support only — verify against a current formulary, NICE, or your local guideline before clinical use.