Fontan Circulation Risk Assessment
Assesses late complications of Fontan circulation in adults and children with single-ventricle physiology. Guides surveillance intensity and intervention timing.
Score interpretation
→ Annual review at ACHD centre; echocardiogram, ECG, liver ultrasound, exercise test; anticoagulation (warfarin or NOAC); healthy lifestyle; prompt treatment of infections
→ Cardiac catheterisation; Fontan conversion planning; diuretics for hepatic congestion; arrhythmia ablation; protein-losing enteropathy treatment (octreotide, budesonide); ACHD centre referral
→ Heart transplant assessment; Fontan conversion to TCPC if appropriate; PDE5 inhibitor for PVR reduction; intensive monitoring; multidisciplinary ACHD team; transplant listing criteria assessment
Interpretation bands for the Fontan Risk. Apply clinical judgement and local guidance.
References
Related
Curated clinical cross-links plus same-class fallbacks.
- Acute Heart Failure · ESC 2021 Heart Failure Guidelines; NICE NG106
- NSTEMI / Unstable Angina · ESC 2020 NSTEMI Guidelines; NICE NG185
- New-Onset Atrial Fibrillation · ESC 2020 AF Guidelines; NICE NG196
- Hypertensive Emergency · ESC/ESH 2018 Hypertension Guidelines; NICE NG136
- Bradycardia Management · Resuscitation Council UK ABCDE; ESC 2021 Pacing Guidelines
- Ventricular Tachycardia / Fibrillation · Resuscitation Council UK ACLS; ESC 2022 Ventricular Arrhythmia Guidelines
Decision support only — verify against a current formulary, NICE, or your local guideline before clinical use.