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Bile acid

Chenodeoxycholic acid

Brand names: Chenodeoxycholic acid Leadiant

Adult dose

Dose: Initial 250mg/day in divided doses; titrate to 750mg/day max divided doses
Route: PO
Frequency: divided

Clinical pearls

  • Cerebrotendinous xanthomatosis (CYP27A1 deficiency) — replaces deficient bile acid

Contraindications

  • Acute biliary inflammation
  • Pregnancy

Side effects

  • Diarrhoea
  • Hepatotoxicity

Interactions

  • Bile acid sequestrants reduce absorption (give 4–6 hours apart)
  • Aluminium-containing antacids reduce absorption

Monitoring

  • LFTs

Reference: BNF; https://bnf.nice.org.uk/drugs/chenodeoxycholic-acid/. Verify against your local formulary and the latest BNF before prescribing.

Related

Curated clinical cross-links plus same-class fallbacks.