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siRNA targeting transthyretin (TTR)

Vutrisiran

Brand names: Amvuttra

Adult dose

Dose: 25mg SC every 3 months
Route: SC
Frequency: q3mo

Clinical pearls

  • Hereditary transthyretin amyloidosis with polyneuropathy
  • Vitamin A 2500 IU/day required; specialist amyloid

Contraindications

  • Hypersensitivity

Side effects

  • Vitamin A deficiency
  • Arthralgia
  • Dyspnoea
  • Injection-site reactions

Monitoring

  • Vitamin A
  • Cardiac function
  • Symptoms

Reference: BNF; NICE HST24; SmPC; https://bnf.nice.org.uk/drugs/vutrisiran/. Verify against your local formulary and the latest BNF before prescribing.

Related

Curated clinical cross-links plus same-class fallbacks.