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rheumatology

Birmingham Vasculitis Activity Score (BVAS)

Measures disease activity in ANCA-associated vasculitis (GPA, MPA, EGPA) across nine organ systems. Guides immunosuppressive therapy.

Score interpretation

Low activity or remission

→ Low disease burden; maintenance immunosuppression; regular monitoring

Moderate active vasculitis

→ Systemic steroids; consider rituximab or cyclophosphamide; organ-specific management

Severe active vasculitis

→ High-dose IV methylprednisolone; rituximab or IV cyclophosphamide; plasma exchange if severe renal disease; monitor for PCP prophylaxis need

Interpretation bands for the BVAS. Apply clinical judgement and local guidance.

References

Related

Curated clinical cross-links plus same-class fallbacks.

Decision support only — verify against a current formulary, NICE, or your local guideline before clinical use.