RheumatologyRenal
Scleroderma Renal Crisis
Acute hypertension + AKI in systemic sclerosis — urgent ACE-I (lifesaving), avoid steroids >15 mg/day.
Source: EULAR 2023; UK Scleroderma Study Group
Step 1 of ~2
info
Recognise
Risk: diffuse cutaneous SSc <4 years from onset, anti-RNA polymerase III antibody, recent corticosteroid (especially >15 mg/day prednisolone). Sudden severe hypertension (often >200/120) + AKI + microangiopathic haemolytic anaemia + thrombocytopenia + headache + visual change + LV dysfunction. Always check BP at every clinical visit in SSc — early detection saves lives.
Related
Curated clinical cross-links plus same-class fallbacks.
Drugs
- Prednisolone (Systemic) · Systemic Corticosteroid — Acute Dermatoses
- Hydralazine (IV — Acute Hypertension in Pregnancy) · Vasodilator (Antihypertensive)
- Mannitol (Osmotic Diuretic — Renal/Neurological) · Acute Oliguric Renal Failure / Raised ICP
- Iloprost (Raynaud's / Systemic Sclerosis) · Prostacyclin Analogue — Vasodilator and Antiplatelet
- Dexamethasone (ICU / ARDS) · Systemic Corticosteroid
- Glyceryl Trinitrate (Sublingual / IV) · Nitrate / Acute Angina
Pathways
- Cutaneous Lupus Erythematosus · BAD; EULAR
- Osteoporosis / Fragility Fracture · NOGG 2021; NICE NG147; NG224
- Arteritic AION (Giant Cell Arteritis) · RCOphth; BSR
- Osteoarthritis Hip / Knee Management · NICE NG226 (2022)
- Lupus Nephritis · EULAR/ERA-EDTA 2019; KDIGO 2024
- Rheumatoid Arthritis Management · NICE CG79 2018 / EULAR 2022
Decision support only. Always apply local guidelines and clinical judgement.